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 Detalle_Publicacion

Granulomatosis with polyangiitis with isolated orbital involvement in children: a case report successfully treated with rituximab and review of the literature

Abstract: We report the case of a 15-year old girl who presented with a non-tender right upper eyelid swelling. Magnetic resonance confirmed the presence of an enlargement of the orbicular muscle with moderate contrast enhancement. Biopsy revealed the presence of necrotizing granulomatous vasculitis. Further studies ruled out systemic involvement. Thus, she was diagnosed with isolated granulomatosis with polyangiitis (GPA). Treatment with steroids and methotrexate was started. Due to the persistence of the lesion, rituximab (RTX) was added with excellent clinical and radiological response. This is, to the best of our knowledge, the first case of isolated orbital GPA treated with RTX in a pediatric patient.

Otras publicaciones de la misma revista o congreso con autores/as de la Universidad de Cantabria

 Fuente: Acta Reumatol Port 2019 Jul 8;44(Jul-Sep (3)):258-263

Editorial: Sociedade Portuguesa de Reumatologia

 Año de publicación: 2019

Nº de páginas: 6

Tipo de publicación: Artículo de Revista

ISSN: 0303-464X

Autores/as

RIANCHO ZARRABEITIA, L.

PEIRÓ CALLIZO, E.

DRAKE PÉREZ, M.

GARCÍA MONTESINOS, B.