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Nusinersen ameliorates motor function and prevents motoneuron Cajal body disassembly and abnormal poly(A) RNA distribution in a SMA mouse model

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Fuente: Sci Rep . 2020 Jul 1;10(1):10738

Publisher: Nature Publishing Group

Publication date: 01/07/2020

No. of pages: 13

Publication type: Article

DOI: 10.1038/s41598-020-67569-3

ISSN: 2045-2322

Spanish project: CB06/05/0037 ; RTI2018-099278-B-I00

Publication Url: https://doi.org/10.1038/s41598-020-67569-3

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Authorship

MARIA TERESA BERCIANO BLANCO

ALBA PUENTE BEDIA

MEDINA MAMAMÉ, ALMUDENA

JOSE CARLOS RODRIGUEZ REY

CALDERÓ, JORDI

MIGUEL ANGEL LAFARGA COSCOJUELA

OLGA TAPIA MARTINEZ

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Nusinersen ameliorates motor function and prevents motoneuron Cajal body disassembly and abnormal poly(A) RNA distribution in a SMA mouse model

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